Image of a neural disease that would cause high-frequency hearing loss.

How frequently do you contemplate your nervous system? For the majority of individuals, the answer would probably be not that often. As long as your body is performing in the way that it should, you have no reason to consider how your neurons are firing or whether nerves are sending proper messages through the electrical pathways of your body. But you tend to take a closer look when something goes wrong and the nerves start to misfire.

There’s one specific condition, known as Charcot-Marie-Tooth (CMT) disease, which can impact the nervous system on a fairly large scale, though the symptoms normally manifest mainly in the extremities. high-frequency hearing loss can also be triggered by CMT according to some evidence.

What Is Charcot-Marie-Tooth Disease?

Charcot-Marie-Tooth disease is a set of inherited conditions. Effectively, these genetic conditions cause something to go wrong with your nerves or with the protective sheathing surrounding your nerves.

This means that the impulses sent from your brain to those nerves (and from those nerves back to your brain) don’t work all that well. A loss of motor function and sensation can be the result.

A combination of genetic elements usually leads to the expression of symptoms, so CMT can be found in several varieties. Symptoms of CMT usually begin in the feet and work their way up to the arms. And, curiously, among those who have CMT, there is a higher rate of occurrence of high-frequency hearing loss.

A Link Between Loss of Hearing And CMT: The Cochlear Nerve

The link between CMT and hearing loss has always been colloquially recognized (that is, everybody knows somebody who has a tells about it – at least inside of the CMT culture). And it was difficult to grasp the link between loss of sensation in the legs and issues with the ears.

The connection was firmly established by a scientific study just recently when a group of researchers examined 79 people with CMT at the University of Iowa Hospitals and Clinics.

The results were rather decisive. Nearly everyone who has CMT passed their low and moderate frequency hearing tests with flying colors. But high-frequency sounds (in the moderate region in particular) were effortlessly heard by all of the participants. According to this research, it seems pretty likely that CMT can at least be associated with high-frequency loss of hearing.

The Cause of Hearing Loss and How to Treat It

The link between high-frequency hearing loss and CMT might, at first, seem perplexing. Like every other part of your body relies on properly functioning nerves. That’s also the same for your ears.

The hypothesis is, CMT affects the cochlear nerve so noises in the high-frequency range aren’t able to be interpreted. Anyone with this type of hearing loss will have a hard time hearing certain sounds, including peoples voices. Trying to understand voices in a crowded noisy room is especially hard.

This kind of hearing loss is commonly managed with hearing aids. There’s no recognized cure for CMT. Modern hearing aids can isolate the precise frequencies to boost which can provide considerable assistance in fighting high-frequency hearing loss. Also, most modern hearing aids can be adjusted to function well inside of noisy surroundings.

Many Factors Behind Hearing Loss

Beyond the untested hypothesis, it’s still uncertain what the connection between CMT and high-frequency hearing loss. But hearing aid tech offers a definite solution to the symptoms of that hearing loss. That’s why many people who have CMT will take the time to get a consultation with a hearing specialist and get fitted for a custom hearing aid.

There are a variety of causes for hearing loss symptoms. Frequently, it’s an issue of loud noise resulting in damage to the ears. In other situations, hearing loss could be the consequence of an obstruction. It also appears that CMT is another possible cause.

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